Table 1 Laboratory data at presentation.

AEoC, absolute eosinophil count; ALC, absolute lymphocyte count; ANC, absolute neutrophil count; n.d.: not done; cpm, counts per minute.

Patient (age)P1
(9 months)
P2
(14 days)
P3
(17 days)
P4
(1 month)
P5
(6 months)
P6
(1 month)
Control
values
ANC (cells × 10−3/μl)0.522.776.361.223.83.961.0–9.0
ALC (cells × 10−3/μl)2.092.182.462.3446.71.553.4–7.6
AEoC (cells × 10−3/μl)5.860.220.670.389.60.860.05–0.7
Platelets (× 10−9/liter)8389667324780449150–400
CD3+ cells/μl1777625843,985182,500–5,500
CD4+ cells/μl1038705010,762181,600–4,000
CD8+ cells/μl291410017,3130560–1,700
CD19+ cells/μl6181,4821,107946936811300–2,000
CD16/56+ cells/μl2083591,1074821,4041,205170–1,100
In vitro proliferation
to PHA (cpm × 10−3)
19.8*5.5n.d.2.162.50.65(≥ 94.9)
IgG (mg/dl)1,450745658690170650611–1,542
IgA (mg/dl)27<6.6<6<25<25<257–37
IgM (mg/dl)21251749117<2526–122
IgE (kU/liter)1,241730<2<210,080<20–9

*Measured as % of CD3+ cells incorporating Edu (normal value: ≥58.5).